Uterus: a Case Report

Primitive neuroectodermal tumors (PNETs) are small round-cell tumors that often show neuroectodermal differentiation. They can be either central or peripheral. Central PNETs are derived from the neural tube predominantly involving the brain or spinal cord. Peripheral PNETs (pPNETs) are derived from the neural crest involving the sympathetic nervous system, bone, or soft tissue [1]. The most common site of pPNET in the female genital tract is the ovary, reported in 27 cases [2–4]. The uterus is the next most common site, with 14 cases reported to date [5]. Cervical, vaginal, and vulvar pPNET are rare, with seven, four, and three cases reported at each primary site, respectively [5–13]. To the best of our knowledge, we report the first case of uterine neuroectodermal tumor in Taiwan. We also review the literature on this topic.